Skin biopsy findings in CADASIL.

نویسندگان

  • Brian W Smith
  • Jean Henneberry
  • Timothy Connolly
چکیده

creased dural venous sinus pressure or a defect in the arachnoid villi. The possibility of dural venous sinus thrombosis was ruled out in this case by MR examination that showed the venous sinuses to be widely patent. As suggested by the MR findings in this patient, low hemoglobin levels may result in compensatory changes in cerebral blood volume, leading to increased intracranial pressure. This case serves as a reminder that an idiopathic intracranial hypertension–like picture may occur as a consequence of severe anemia and is reversible upon correction of the underlying hematologic disorder. In addition, this case underscores the fact that idiopathic intracranial hypertension may presage the onset of systemic lupus erythematosus.

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عنوان ژورنال:
  • Neurology

دوره 59 6  شماره 

صفحات  -

تاریخ انتشار 2002